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一名患有I型假性醛固酮减少症的儿童出现复发性铜绿假单胞菌支气管肺炎及其他类似囊性纤维化的症状。

Recurrent Pseudomonas bronchopneumonia and other symptoms as in cystic fibrosis in a child with type I pseudohypoaldosteronism.

作者信息

Marthinsen L, Kornfält R, Aili M, Andersson D, Westgren U, Schaedel C

机构信息

Department of Paediatrics, Halmstad Hospital, Sweden.

出版信息

Acta Paediatr. 1998 Apr;87(4):472-4.

PMID:9628311
Abstract

We report a child with multiple target organ pseudohypoaldosteronism type 1 with frequent recurrent pulmonary infections caused by Pseudomonas aeruginosa and Pasteurella multocida and high levels of chloride in sweat, urine and nasal secretion. Repetitive faecal chymotrypsin samples have all shown pathological values in spite of no other sign of exocrine pancreas dysfunction. The similarities with cystic fibrosis and the importance of the salt content in bronchial fluid are discussed.

摘要

我们报告了一名患有1型多靶器官假性醛固酮减少症的儿童，该患儿频繁反复发生由铜绿假单胞菌和多杀巴斯德菌引起的肺部感染，且汗液、尿液和鼻腔分泌物中的氯含量较高。尽管没有其他外分泌胰腺功能障碍的迹象，但多次粪便糜蛋白酶样本均显示出病理值。文中讨论了与囊性纤维化的相似之处以及支气管液中盐分含量的重要性。

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