Juang J M, Silva A C, Pires M C, Valente N Y, Sittart J A
Serviço de Dermatologia, Hospital do Servidor Público Estadual de São Paulo.
Rev Assoc Med Bras (1992). 1998 Jan-Mar;44(1):50-2. doi: 10.1590/s0104-42301998000100010.
The neurocutaneous melanosis is a rare syndrome in which the congenital melanocytic nevi and excessive melanosis are the main features. The syndrome seems to be a morphogenesis error of the embryonic neuroectoderm. A clinical case with necroscopy in a 19 year-old man who had developed malign melanoma in his central nervous system is reported.
神经皮肤黑素沉着症是一种罕见的综合征,其主要特征为先天性黑素细胞痣和黑素沉着过多。该综合征似乎是胚胎神经外胚层的形态发生错误。本文报道了一例19岁男性的临床病例及尸检情况,该患者在中枢神经系统发生了恶性黑色素瘤。