Kroes E J, Festen C
Department of Paediatric Surgery, St. Radboud Hospital, Nijmegen, The Netherlands.
Pediatr Surg Int. 1998 Jul;13(5-6):416-8. doi: 10.1007/s003830050353.
Congenital microgastria is an uncommon result of impairment of normal foregut development. To date, only 39 cases have been described in the literature. We report a boy born with microgastria and bilateral hypoplastic kidneys who had feeding problems, resulting in failure to thrive and growth retardation. After a short period of conservative management, he was operated upon at the age of 11 months. A Hunt-Lawrence pouch was created, leading to toleration of increasing amounts of oral feeding. Although his feeding problems have decreased, his height and weight are below normal (<10th percentile). The embryology, clinical presentation, diagnostic procedures, associated anomalies, and management are discussed.
先天性小胃是正常前肠发育受损的罕见结果。迄今为止,文献中仅描述了39例。我们报告了一名患有小胃和双侧肾发育不全的男孩,他存在喂养问题,导致发育不良和生长迟缓。经过短期保守治疗后,他在11个月大时接受了手术。制作了一个亨特-劳伦斯袋,使他能够耐受逐渐增加的经口喂养量。尽管他的喂养问题有所减轻,但他的身高和体重仍低于正常水平(<第10百分位数)。本文讨论了其胚胎学、临床表现、诊断方法、相关异常及治疗。