病例报告：表现为巨十二指肠的自发性孤立性肠系膜纤维瘤病

Case report: Spontaneous isolated mesenteric fibromatosis presenting as megaduodenum.

作者信息

Chen Y J, Tam K W, Chen C S, Wu C H, Chen S C, Chan W P, Fang C L, Liu J D, Pan S

机构信息

Department of Surgery, Taipei Medical College Hospital, Taiwan.

出版信息

J Gastroenterol Hepatol. 1998 Apr;13(4):383-6. doi: 10.1111/j.1440-1746.1998.tb00650.x.

DOI:10.1111/j.1440-1746.1998.tb00650.x

PMID:9641301

Abstract

A case of spontaneous isolated mesenteric fibromatosis presenting as megaduodenum is reported. The lesion was small, only 2 cm in its greatest diameter. However, because of its location near the ligament of Treitz and because of its characteristic infiltrative growth pattern, the tumour involved the distal duodenum and resulted in acute angulation and obstruction early in its course. We successfully resected the mass and the patient is in fair physical condition 6 months after operation.

摘要

报告了一例表现为巨十二指肠的自发性孤立性肠系膜纤维瘤病病例。病变较小，最大直径仅2厘米。然而，由于其位于Treitz韧带附近且具有特征性的浸润性生长模式，肿瘤累及十二指肠远端，并在病程早期导致急性成角和梗阻。我们成功切除了肿块，患者术后6个月身体状况良好。