Mohand-Said S, Deudon-Combe A, Hicks D, Simonutti M, Forster V, Fintz A C, Léveillard T, Dreyfus H, Sahel J A
Laboratoire de Physiopathologie Rétinienne, Université Louis Pasteur, Clinique Ophtalmologique, Centre Hospitalier et Universitaire, BP 426, 1, Place de l'Hôpital, 67091 Strasbourg Cedex, France.
Proc Natl Acad Sci U S A. 1998 Jul 7;95(14):8357-62. doi: 10.1073/pnas.95.14.8357.
The role of cellular interactions in the mechanism of secondary cone photoreceptor degeneration in inherited retinal degenerations in which the mutation specifically affects rod photoreceptors was studied. We developed an organ culture model of whole retinas from 5-week-old mice carrying the retinal degeneration mutation, which at this age contain few remaining rods and numerous surviving cones cocultured with primary cultures of mixed cells from postnatal day 8 normal-sighted mice (C57BL/6) retinas or retinal explants from normal (C57BL/6) or dystrophic (C3H/He) 5-week-old mice. After 7 days, the numbers of residual cone photoreceptors were quantified after specific peanut lectin or anti-arrestin antibody labeling by using an unbiased stereological approach. Examination of organ cultured retinas revealed significantly greater numbers of surviving cones (15-20%) if cultured in the presence of retinas containing normal rods as compared with controls or cocultures with rod-deprived retinas. These data indicate the existence of a diffusible trophic factor released from retinas containing rod cells and acting on retinas in which only cones are present. Because cones are responsible for high acuity and color vision, such data could have important implications not only for eventual therapeutic approaches to human retinal degenerations but also to define interactions between retinal photoreceptor types.
研究了细胞间相互作用在遗传性视网膜变性继发性视锥光感受器变性机制中的作用,在这些遗传性视网膜变性中,突变特异性地影响视杆光感受器。我们建立了一个器官培养模型,该模型采用来自携带视网膜变性突变的5周龄小鼠的全视网膜,在这个年龄段,剩余的视杆细胞很少,而有大量存活的视锥细胞,将其与来自出生后第8天正常视力小鼠(C57BL/6)视网膜的混合细胞原代培养物或来自正常(C57BL/6)或营养不良(C3H/He)5周龄小鼠的视网膜外植体共培养。7天后,通过无偏立体学方法,在特定花生凝集素或抗抑制蛋白抗体标记后,对视锥光感受器的残留数量进行定量。对器官培养视网膜的检查显示,如果与含有正常视杆细胞的视网膜一起培养,存活的视锥细胞数量(15%-20%)比对照组或与缺乏视杆细胞的视网膜共培养时显著增加。这些数据表明,存在一种可扩散的营养因子,它从含有视杆细胞的视网膜释放出来,并作用于仅存在视锥细胞的视网膜。由于视锥细胞负责高敏锐度和色觉,这些数据不仅可能对人类视网膜变性的最终治疗方法具有重要意义,而且对于定义视网膜光感受器类型之间的相互作用也具有重要意义。