Howlin P, Davies M, Udwin O
Department of Psychology, St George's Hospital Medical School, London, U.K.
J Child Psychol Psychiatry. 1998 Feb;39(2):183-9.
This paper reports the results of cognitive, linguistic, and academic assessments in a representative sample of 62 adults with Williams syndrome. The average age of the group was 26 years and their mean full scale IQ was 61. Differences between Verbal and Performance IQ, and between receptive and expressive language skills, were smaller than generally found in studies of children with this condition. However, an examination of subtest scores revealed an almost identical cognitive profile to that found in children. Skills in other areas, such as reading, spelling, arithmetic, and social adaptation remained at a low level, with functioning generally being around a 6-8-year age equivalent. The consistency of reports on intellectual abilities in both child and adult studies of individuals with Williams syndrome lends increased support to the notion of a syndrome specific pattern of cognitive, linguistic, and adaptive functioning.
本文报告了对62名威廉姆斯综合征成年患者代表性样本进行认知、语言和学业评估的结果。该组的平均年龄为26岁，平均全量表智商为61。言语智商和操作智商之间以及接受性和表达性语言技能之间的差异，比在患有这种疾病的儿童研究中通常发现的要小。然而，对分测验分数的检查显示，其认知概况与在儿童中发现的几乎相同。其他领域的技能，如阅读、拼写、算术和社会适应能力仍处于较低水平，功能通常相当于6至8岁儿童的水平。在威廉姆斯综合征患者的儿童和成人研究中，关于智力能力报告的一致性，为存在特定综合征的认知、语言和适应性功能模式这一观点提供了更多支持。
