Kiliçarslan B, Yaz M, Paksoy N
Department of Patholoogy, Akdeniz University Faculty of Medicine, Antalya, Turkey.
Turk J Pediatr. 1998 Apr-Jun;40(2):289-94.
Congenital cystic adenomatoid malformation (CCAM) of the lung is a rare pulmonary lesion, characterized by an excessive overgrowth of the terminal respiratory bronchioles. The lesion is almost always unilateral and may occur in any lobe. We present two children with CCAM. The first case was a one-day-old female infant admitted with respiratory distress and cyanosis. The second case was a 19-month-old girl with a nine-month history of recurrent respiratory infections. Preoperative diagnosis of both cases was intrapulmonary mass. The histopathological examinations revealed CCAM.
先天性肺囊性腺瘤样畸形（CCAM）是一种罕见的肺部病变，其特征为终末呼吸细支气管过度增生。该病变几乎总是单侧的，可发生于任何肺叶。我们报告两例CCAM患儿。第一例是一名1日龄女婴，因呼吸窘迫和发绀入院。第二例是一名19个月大的女孩，有9个月反复呼吸道感染病史。两例术前诊断均为肺内肿块。组织病理学检查显示为CCAM。
