门克斯病蛋白ATP7A中铜结合位点的研究。SSIEM奖。先天性代谢缺陷研究学会。 - Suppr

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超能文献

Investigation of the copper binding sites in the Menkes disease protein, ATP7A. SSIEM Award. Society of the Study of Inborn Errors of Metabolism.

作者信息

Jensen P Y, Bonander N, Karlsson B G, Horn N, Tümer Z, Farver O

机构信息

Department of Analytical and Pharmaceutical Chemistry, Royal Danish School of Pharmacy, Copenhagen, Denmark.

出版信息

J Inherit Metab Dis. 1998 Jun;21(3):195-8. doi: 10.1023/a:1005331130245.

DOI:10.1023/a:1005331130245

PMID:9686355

Abstract

摘要

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本文引用的文献

Structures of the reduced and mercury-bound forms of MerP, the periplasmic protein from the bacterial mercury detoxification system.

Biochemistry. 1997 Jun 10;36(23):6885-95. doi: 10.1021/bi9631632.

Immunocytochemical localization of the Menkes copper transport protein (ATP7A) to the trans-Golgi network.

Hum Mol Genet. 1997 Mar;6(3):409-16. doi: 10.1093/hmg/6.3.409.

Copper transport and its alterations in Menkes and Wilson diseases.

Biochim Biophys Acta. 1997 Feb 27;1360(1):3-16. doi: 10.1016/s0925-4439(96)00064-6.

Ligand-regulated transport of the Menkes copper P-type ATPase efflux pump from the Golgi apparatus to the plasma membrane: a novel mechanism of regulated trafficking.

EMBO J. 1996 Nov 15;15(22):6084-95.

ATP-dependent copper transporter, in the Golgi apparatus of rat hepatocytes, transports Cu(II) not Cu(I).

Am J Physiol. 1996 Nov;271(5 Pt 1):G741-6. doi: 10.1152/ajpgi.1996.271.5.G741.

Biochemical characterization and intracellular localization of the Menkes disease protein.

Proc Natl Acad Sci U S A. 1996 Nov 26;93(24):14030-5. doi: 10.1073/pnas.93.24.14030.

Menkes disease: recent advances and new insights into copper metabolism.

Ann Med. 1996 Apr;28(2):121-9. doi: 10.3109/07853899609092936.

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