Kakura H, Miyahara K, Sohara H, Amitani S, Koga M, Moriyama Y, Taira A
Division of Cardiology, Shinkyo Hospital, Kagoshima, Japan.
Jpn Heart J. 1998 Mar;39(2):235-41. doi: 10.1536/ihj.39.235.
We evaluated a 68-year-old male patient with isolated levocardia without intracardiac anomaly. The patient's condition was complicated by the absence of the inferior vena cava, a lobulated spleen and sick sinus syndrome. Isolated levocardia without intracardiac anomaly is very rare and only 25 cases of this disease have been reported, to our knowledge. In general, it is accepted that cardiac rhythm disorder is frequently observed in cases of isolated levocardia and/or absence of inferior vena cava. However, there are few cases of isolated levocardia without intracardiac anomaly complicated by the absence of the inferior vena cava, a lobulated spleen and apparent sick sinus syndrome.
我们评估了一名68岁男性患者，其心脏左旋，无心脏内异常。患者的病情因下腔静脉缺如、分叶状脾脏和病态窦房结综合征而复杂化。据我们所知，心脏左旋且无心脏内异常的情况非常罕见，仅报告过25例这种疾病。一般来说，人们公认在心脏左旋和/或下腔静脉缺如的病例中经常观察到心律失常。然而，心脏左旋且无心脏内异常，同时合并下腔静脉缺如、分叶状脾脏和明显病态窦房结综合征的病例却很少见。
