人类疾病动物模型：C型尼曼-匹克病 - Suppr

Suppr

超能文献

Animal model of human disease: Niemann-Pick Disease type C.

作者信息

Adachi M, Volk B W, Schneck L

出版信息

Am J Pathol. 1976 Oct;85(1):229-32.

PMID:970440

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2032539/

Abstract

摘要

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff01/2032539/f8f6ca5a21ad/amjpathol00443-0241-a.jpg

相似文献

Animal model of human disease: Niemann-Pick Disease type C.人类疾病动物模型：C型尼曼-匹克病

Am J Pathol. 1976 Oct;85(1):229-32.

Cholesterol accumulation and liver cell death in mice with Niemann-Pick type C disease.尼曼-匹克C型病小鼠的胆固醇蓄积与肝细胞死亡

Hepatology. 2005 Oct;42(4):886-93. doi: 10.1002/hep.20868.

Axonal dystrophy of dorsal root ganglion sensory neurons in a mouse model of Niemann-Pick disease type C.尼曼-匹克病C型小鼠模型中背根神经节感觉神经元的轴突营养不良

Exp Neurol. 2004 Jun;187(2):289-98. doi: 10.1016/j.expneurol.2004.03.002.

Neuroglial activation in Niemann-Pick Type C mice is suppressed by intracerebral transplantation of bone marrow-derived mesenchymal stem cells.骨髓源性间充质干细胞脑内移植可抑制尼曼-匹克C型小鼠的神经胶质细胞激活。

Neurosci Lett. 2005 Jun 24;381(3):234-6. doi: 10.1016/j.neulet.2005.02.029. Epub 2005 Mar 3.

Diffusion tensor imaging in Niemann-Pick Type C disease.尼曼-匹克C型病的扩散张量成像

Pediatr Neurol. 2005 Nov;33(5):325-30. doi: 10.1016/j.pediatrneurol.2005.05.004.

Tamoxifen and vitamin E treatments delay symptoms in the mouse model of Niemann-Pick C.

J Appl Genet. 2004;45(4):461-7.

Niemann-Pick disease. Sphingomyelinosis of Siamese cats.尼曼-匹克病。暹罗猫的鞘磷脂沉积病。

Am J Pathol. 1982 Aug;108(2):252-4.

Defective calcium homeostasis in the cerebellum in a mouse model of Niemann-Pick A disease.尼曼-匹克病A型小鼠模型中，小脑钙稳态失调。

J Neurochem. 2005 Dec;95(6):1619-28. doi: 10.1111/j.1471-4159.2005.03534.x. Epub 2005 Nov 8.

Postnatal development of inflammation in a murine model of Niemann-Pick type C disease: immunohistochemical observations of microglia and astroglia.尼曼-匹克C型病小鼠模型中产后炎症的发展：小胶质细胞和星形胶质细胞的免疫组织化学观察

Exp Neurol. 2003 Dec;184(2):887-903. doi: 10.1016/S0014-4886(03)00345-5.

Patterned Purkinje cell degeneration in mouse models of Niemann-Pick type C disease.尼曼-匹克C型病小鼠模型中的浦肯野细胞模式性变性。

J Comp Neurol. 2003 Feb 10;456(3):279-91. doi: 10.1002/cne.10522.

引用本文的文献

Mass spectrometry-based proteomics in neurodegenerative lysosomal storage disorders.基于质谱的神经退行性溶酶体贮积症蛋白质组学。

Mol Omics. 2022 May 11;18(4):256-278. doi: 10.1039/d2mo00004k.

The Cerebellum in Niemann-Pick C1 Disease: Mouse Versus Man.尼曼-匹克C1病中的小脑：小鼠与人类的对比

Cerebellum. 2023 Feb;22(1):102-119. doi: 10.1007/s12311-021-01347-3. Epub 2022 Jan 18.

Differential Proteomics Reveals miR-155 as a Novel Indicator of Liver and Spleen Pathology in the Symptomatic Niemann-Pick Disease, Type C1 Mouse Model.差异蛋白质组学揭示 miR-155 作为尼曼-匹克病 C1 型症状小鼠模型肝脾病理学的新型指标。

Molecules. 2019 Mar 12;24(5):994. doi: 10.3390/molecules24050994.

Lysosomal enzyme replacement therapies: Historical development, clinical outcomes, and future perspectives.溶酶体酶替代疗法：历史发展、临床结果和未来展望。

Adv Drug Deliv Rev. 2017 Sep 1;118:109-134. doi: 10.1016/j.addr.2017.05.004. Epub 2017 May 11.

Type C Niemann-Pick disease in a boxer dog.

Acta Neuropathol. 1993;85(3):345-8. doi: 10.1007/BF00227733.

Niemann-Pick disease. Sphingomyelinosis of Siamese cats.尼曼-匹克病。暹罗猫的鞘磷脂沉积病。

Am J Pathol. 1982 Aug;108(2):252-4.

Neurovisceral sphingomyelinosis in a Siamese cat.

Acta Neuropathol. 1989;79(3):330-2. doi: 10.1007/BF00294670.

Feline sphingolipidosis resembling Niemann-Pick disease type C.

Acta Neuropathol. 1990;81(2):189-97. doi: 10.1007/BF00334507.

Progress in investigations of sphingolipidoses.鞘脂类贮积病的研究进展

Acta Neuropathol. 1978 Aug 7;43(1-2):1-18. doi: 10.1007/BF00684994.

本文引用的文献

FORM-CELL RETICULOSIS OF MICE: AN INHERITED CONDITION RESEMBLING GAUCHER'S AND NIERMANN-PICK DISEASES.小鼠的泡沫细胞网状细胞增多症：一种类似高雪氏病和尼曼-皮克病的遗传性疾病。

J Med Genet. 1965 Jun;2(2):99-106. doi: 10.1136/jmg.2.2.99.

The cerebral defect in Tay-Sachs disease and Niemann-Pick disease.泰-萨克斯病和尼曼-匹克病中的脑缺陷。

J Neurochem. 1961 Apr;7:69-80. doi: 10.1111/j.1471-4159.1961.tb13499.x.

Sphingomyelinase in normal human spleens and in spleens from subjects with Niemann-Pick disease.正常人脾脏及尼曼-匹克病患者脾脏中的鞘磷脂酶

J Lipid Res. 1967 May;8(3):202-9.

Quantitative determination of lysolecithin and sphingomyelin in phospholipid mixtures by thin-layer chromatography as applied to the thymus of the fmfm mouse.应用于fmfm小鼠胸腺的磷脂混合物中溶血卵磷脂和鞘磷脂的薄层色谱法定量测定

J Lipid Res. 1974 May;15(3):283-5.

The central nervous system, liver, and spleen of FM mice. Ultrastructural, histochemical, and biochemical studies.FM小鼠的中枢神经系统、肝脏和脾脏。超微结构、组织化学和生物化学研究。

Arch Pathol. 1974 Apr;97(4):232-8.

Lipid abnormalities in foam cell reticulosis of mice, an analogue of human sphingomyelin lipidosis.小鼠泡沫细胞网状细胞增多症中的脂质异常，人类鞘磷脂沉积症的类似物。

J Lipid Res. 1969 May;10(3):288-93.

文献AI研究员

20分钟写一篇综述，助力文献阅读效率提升50倍。

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索

文档翻译

学术文献翻译模型，支持多种主流文档格式。

立即体验