Ng S C, Lee B W, Chia F
Department of Paediatrics, National University Hospital, Singapore.
Singapore Med J. 1998 May;39(5):211-6.
Idiopathic pulmonary haemosiderosis (IPH) is a disorder characterised by the triad of haemoptysis, diffuse parenchymal infiltrates on chest roentgenogram and iron-deficiency anaemia. It is a diagnosis of exclusion and the prognosis is bleak despite the varied management options. We report a case of IPH occurring in a child who presented at four months of age with cough, wheeze, haemoptysis and pallor and whose symptoms are currently controlled with high-dose inhaled budesonide and low-dose oral prednisolone.
特发性肺含铁血黄素沉着症(IPH)是一种以咯血、胸部X线片显示弥漫性实质性浸润和缺铁性贫血三联征为特征的疾病。它是一种排除性诊断,尽管有多种治疗选择,但其预后不佳。我们报告一例IPH患儿,该患儿4个月大时出现咳嗽、喘息、咯血和面色苍白,目前其症状通过高剂量吸入布地奈德和低剂量口服泼尼松龙得到控制。