Le Cam M T, Wolkenstein P, Cosnes A, Bocquet H, Gaulard P, Tulliez M, Cordonnier C, Roujeau J C, Bagot M, Revuz J
Service de Dermatologie, Hôpital Henri-Mondor, Créteil.
Ann Dermatol Venereol. 1997;124(9):621-2.
Acute mast cell leukemia is a rare and severe disease. We report herein a case associated with a flush syndrome.
A 44-year-old man, presented with a flush of face and trunk. Bone marrow was infiltrated with immature mast cells. In spite of chemotherapy and bone marrow transplantation the patient deceased.
Pheochromocytoma, carcinoid tumor, and mastocytosis are associated with a flush syndrome. In our patient the diagnosis was an acute mast cell leukemia. Acute mast cell leukemia can follow systemic mastocytosis or occur de novo. This disease is of poor prognosis. No treatment is available.
急性肥大细胞白血病是一种罕见且严重的疾病。我们在此报告一例与潮红综合征相关的病例。
一名44岁男性，出现面部和躯干潮红。骨髓被未成熟肥大细胞浸润。尽管进行了化疗和骨髓移植，患者仍死亡。
嗜铬细胞瘤、类癌肿瘤和肥大细胞增多症与潮红综合征相关。在我们的患者中，诊断为急性肥大细胞白血病。急性肥大细胞白血病可继发于系统性肥大细胞增多症或原发发生。这种疾病预后较差。尚无有效的治疗方法。
