García Muret M P, Pujol R M, de Moragas J M
Clínica Quirón, Barcelona, España.
Ann Dermatol Venereol. 1998 May;125(5):325-7.
Multiple facial angiofibromas are considered a characteristic and pathognomonic feature of tuberous sclerosis. In contrast, the observation of localized multiple angiofibromas limited to one side of the face is a uncommon.
We cared for two patients with multiple clustered unilateral angiofibromas (although one patient also presented a few angiofibromas on the other side) without other features associated with the sclerosis tuberous complex.
The possibility that these patients presented an independent disorder or a minor form of tuberous sclerosis is discussed.
多发性面部血管纤维瘤被认为是结节性硬化症的一个特征性和诊断性特征。相比之下，局限性多发性血管纤维瘤局限于面部一侧的情况并不常见。
我们诊治了两名患有多发性簇状单侧血管纤维瘤的患者（尽管其中一名患者在另一侧也有一些血管纤维瘤），且无其他与结节性硬化症相关的特征。
讨论了这些患者出现独立疾病或结节性硬化症轻微形式的可能性。
