Babatasi G, Massetti M, Saloux E, Grollier G, Agostini D, Potier J C, Khayat A
Service de chirurgie thoracique et cardiovasculaire, CHU Caen.
Arch Mal Coeur Vaiss. 1998 Jan;91(1):83-6.
Dissection of the aorta is a serious condition but rare in young women, and occurring during the 3rd trimester of pregnancy. The main risk factors are hypertension and diseases of the connective tissue or of collagen (Marfan's syndrome and Ehlers-Danlos disease). The authors report a case of dissection of the aorta managed in a pluridisciplinary manner by the anaesthetists, cardiologists, obstetricians and cardiothoracic surgeons, which resulted in a favourable outcome for both mother and baby. The diagnosis of Ehlers-Danlos disease was made from the onset and, over a period of 10 years with CT scan and annual echocardiographic follow-up, total replacement of the supra-coronary aorta was performed in several stages.
主动脉夹层是一种严重疾病，但在年轻女性中罕见，且发生于妊娠晚期。主要危险因素为高血压以及结缔组织或胶原蛋白疾病（马凡综合征和埃勒斯-当洛综合征）。作者报告了一例主动脉夹层病例，由麻醉师、心脏病专家、产科医生和心胸外科医生以多学科方式进行治疗，母婴均获得良好结局。埃勒斯-当洛综合征自发病起即被诊断，在10年期间通过CT扫描和每年的超声心动图随访，分阶段对冠状动脉上方的主动脉进行了全置换。
