Scola R H, Iwamoto F M, Ramos C S, Sanderson A M, Lopardo D, Cantarelli A, Watanabe M, Horta W, Werneck L C
Serviço de Doenças Neuromusculares do Hospital de Clínicas da Universidade Federal do Paraná, Brasil.
Arq Neuropsiquiatr. 1998 Sep;56(3A):457-64. doi: 10.1590/s0004-282x1998000300017.
Two cases of Lambert-Eaton myasthenic syndrome, in female patients whose neoplasm investigation was negative, are reported. Repetitive stimulation of ulnar nerve showed an incremental response (+187% and +198%). Needle EMG was normal in one of them, however, the other patient showed fibrillation potentials, positive sharp waves, potentials of low amplitude and short duration. The authors discuss the clinical, electrophysiological, and pathological features of the disease, as well as some aspects of the treatment and follow-up of these patients.
报告了两例兰伯特-伊顿肌无力综合征病例,患者均为女性,肿瘤检查呈阴性。对尺神经进行重复刺激显示递增反应(分别为+187%和+198%)。其中一例患者针极肌电图正常,然而,另一例患者出现纤颤电位、正锐波、低振幅和短时限电位。作者讨论了该疾病的临床、电生理和病理特征,以及这些患者治疗和随访的一些方面。