Hadjadj E, Conrath J, Ridings B, Denis D
Service d'Ophtalmologie du Pr D. Denis, Centre Hospitalo-Universitaire Nord, Marseille.
J Fr Ophtalmol. 1998 Apr;21(4):276-82.
Brown's syndrome is a form of anatomical strabismus, or retraction syndrome. It is defined by active and passive limitation of upward gaze in adduction in the field of action of the inferior oblique muscle. The etiology of Brown's syndrome remains unknown. The defect lies at the level of the superior oblique's tendonis trajectory via the trochlea. We studied the frequency of clinical signs and results after surgery in patients presenting congenital Brown's syndrome.
Our study involved 18 children. They all underwent complete ophthalmological examination with orthoptic testing, pre and postoperatively.
Neither sidedness nor predominance of sex was noted. Compensatory head posture was noted in 7 of 18 cases. Limitation of upward gaze in adduction was a constant finding, with a positive duction test. Eleven cases underwent superior oblique recession. Results of surgery were satisfactory, with resolution of compensatory head posture in over 80% of cases.
The etiology of congenital Brown's syndrome remains unknown. The different surgical techniques give inconstant results. Operative indication is decided only when in the presence of well defined clinical manifestations: CHP, deviation in primary position with alteration of binocular vision.
布朗综合征是一种解剖性斜视或眼球后退综合征。它由下斜肌作用域内内收时向上注视的主动和被动受限所定义。布朗综合征的病因尚不清楚。缺陷位于上斜肌腱通过滑车的轨迹水平。我们研究了先天性布朗综合征患者的临床体征频率及手术效果。
我们的研究纳入了18名儿童。他们均在术前和术后接受了包括斜视检查在内的全面眼科检查。
未发现明显的左右侧差异及性别优势。18例中有7例出现代偿头位。内收时向上注视受限是持续存在的表现,牵拉试验阳性。11例接受了上斜肌后徙术。手术效果满意,超过80%的病例代偿头位得到矫正。
先天性布朗综合征的病因尚不清楚。不同的手术技术效果不一。仅在存在明确的临床表现(代偿头位、原在位斜视伴双眼视觉改变)时才决定手术指征。