Goris H, Heindryckx E, Van Hoe L, Stockx L, Marchal G, Deceuninck M
Department of Radiology, University Hospitals, Leuven, Belgium.
J Belge Radiol. 1998 Aug;81(4):184-5.
Osler-Rendu-Weber disease, or hereditary hemorrhagic telangiectasia, is a vascular disease with autosomal dominant transmission. The liver is involved in 31% of patients with hereditary hemorrhagic telangiectasia (1). It appears that the lesions uncommonly causes serious disease. We report the imaging findings and the therapy in a case with extensive telangiectasis in the liver.
奥斯勒-伦杜-韦伯病,即遗传性出血性毛细血管扩张症,是一种常染色体显性遗传的血管疾病。遗传性出血性毛细血管扩张症患者中31%会累及肝脏(1)。这些病变似乎很少引发严重疾病。我们报告一例肝脏广泛毛细血管扩张症患者的影像学表现及治疗情况。