Prahlow J A, Barnard J J, Milewicz D M
Southwestern Institute of Forensic Sciences, Dallas, TX, USA.
J Forensic Sci. 1998 Nov;43(6):1244-9.
Rupture of thoracic aortic aneurysms and/or dissections is not rare, occurring in approximately 0.6% of all medicolegal autopsies. Most forensic pathologists are aware of the association between thoracic aortic aneurysms/dissections and trauma, atherosclerosis, inflammation and Marfan syndrome. In this report, we discuss a familial form of thoracic aortic dilatation and/or dissection that is distinct from Marfan syndrome. In addition, we review the topic of thoracic aortic aneurysm and dissection and encourage family notification by forensic pathologists when familial forms of aortic disease are suspected at autopsy.
胸主动脉瘤和/或夹层破裂并不罕见，约占所有法医尸检的0.6%。大多数法医病理学家都知道胸主动脉瘤/夹层与创伤、动脉粥样硬化、炎症和马凡综合征之间的关联。在本报告中，我们讨论一种与马凡综合征不同的家族性胸主动脉扩张和/或夹层形式。此外，我们回顾了胸主动脉瘤和夹层的主题，并鼓励法医病理学家在尸检时怀疑存在家族性主动脉疾病形式时通知家属。
