Leccisotti S, Eramo S, Palattella P, Dolci G
Istituto di Clinica Odontoiatrica, Università degli Studi di Roma La Sapienza.
Minerva Stomatol. 1998 Oct;47(10):545-51.
Radicular dentin dysplasia (DD-I) is a rare hereditary dental alteration. It is characterized clinically by almost normal looking crowns and severe hypermobility of the teeth. The radiographic analysis, on the other hand, discloses the obliteration of all pulp chambers, the short, malformed roots and plenty of periapical bone radiolucencies on noncarious teeth. A case of radicular dentin dysplasia is presented. In this 43-year-old woman the diagnosis was supported, besides the clinical and radiographic analysis, by the pedigree of the proband, which showed the autosomal dominant pattern of feature transmission. Further-more, the electron microscopic analysis of one extracted molar revealed the atubular structure of the secondary dentin, and its globular organization.
根端牙本质发育异常（DD-I型）是一种罕见的遗传性牙齿病变。其临床特征为牙冠外观几乎正常，但牙齿严重松动。另一方面，影像学分析显示所有牙髓腔闭锁、牙根短且形态异常，以及非龋性牙齿有大量根尖周骨质透射区。本文报告了一例根端牙本质发育异常病例。在这位43岁女性患者中，除临床和影像学分析外，先证者的家系显示特征传递为常染色体显性模式，支持了诊断。此外，对一颗拔除磨牙的电子显微镜分析揭示了继发性牙本质的无小管结构及其球状组织。
