Sahoo Sujit Ranjan, Aggarwal Sonia
Department of Conservative Dentistry and Endodontics, Institute of Dental sciences and Hospital, SOA University Bhubaneswar, Odisha, India.
Indian J Dent Res. 2014 Nov-Dec;25(6):832-4. doi: 10.4103/0970-9290.152217.
Dentin dysplasia is a rare hereditary disturbance of dentin formation characterized by a defective dentin development with clinically normal-appearing crowns, severe hypermobility of teeth and spontaneous dental abscesses or cysts. Radiographic analysis shows obliteration of all pulp chambers by pulp stones, short, blunted and malformed or absent roots, peri-apical radiolucencies of noncarious teeth. We present a case of dentin dysplasia type 1d in a 19-year-old boy along with the clinical, radiographic findings of this condition and treatment. There are still many inconclusive issues in the diagnosis and management of patients with dentin dysplasia. The diagnostic features of this rare disturbance will remain incompletely defined until additional cases have been described.
牙本质发育异常是一种罕见的牙本质形成遗传性紊乱疾病，其特征为牙本质发育缺陷，牙冠外观正常，牙齿严重松动，以及自发性牙脓肿或囊肿。影像学分析显示，牙髓腔被牙髓石完全闭塞，牙根短、钝、畸形或缺失，非龋性牙齿根尖周有透射区。我们报告一例19岁男孩的1d型牙本质发育异常病例，并介绍该疾病的临床、影像学表现及治疗情况。牙本质发育异常患者的诊断和管理仍存在许多不确定问题。在描述更多病例之前，这种罕见疾病的诊断特征仍将不完全明确。
