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血栓性血小板减少性紫癜——脾切除术后缓解。病例报告及文献复习。

Thrombotic thrombocytopenic purpura--remission following splenectomy. Report of a case and review of the literature.

作者信息

Reynolds P M, Jackson J M, Brine J A, Vivian A B

出版信息

Am J Med. 1976 Sep;61(3):439-47. doi: 10.1016/0002-9343(76)90385-5.

DOI:10.1016/0002-9343(76)90385-5
PMID:986764
Abstract

A case of thrombotic thrombocytopenic purpura in which sustained remission followed splenectomy is described. Strong serologic evidence of concurrent infection with Mycoplasma pneumoniae was found in this case. Previously reported cases in which thrombotic thrombocytopenic purpura has been associated with infections are reviewed. An approach to management of this unusual and frequently fetal condition, is suggested, based on a detailed review of the recent literature.

摘要

本文描述了一例血栓性血小板减少性紫癜患者,该患者在脾切除术后实现了持续缓解。此病例中发现了肺炎支原体并发感染的有力血清学证据。对先前报道的血栓性血小板减少性紫癜与感染相关的病例进行了综述。基于对近期文献的详细回顾,提出了一种针对这种不寻常且常危及生命状况的治疗方法。

相似文献

1
Thrombotic thrombocytopenic purpura--remission following splenectomy. Report of a case and review of the literature.血栓性血小板减少性紫癜——脾切除术后缓解。病例报告及文献复习。
Am J Med. 1976 Sep;61(3):439-47. doi: 10.1016/0002-9343(76)90385-5.
2
Treatment of thrombotic thrombocytopenic purpura with antiplatelet drugs.用抗血小板药物治疗血栓性血小板减少性紫癜。
Blood. 1973 Jul;42(1):27-33.
3
Thrombotic thrombocytopenic purpura in a previously splenectomized patient.
Am J Med. 1976 Jun;60(7):1061-3. doi: 10.1016/0002-9343(76)90581-7.
4
Thrombotic thrombocytopenic purpura: combined treatment with plasmapheresis and antiplatelet agents.血栓性血小板减少性紫癜:血浆置换与抗血小板药物联合治疗
Ann Intern Med. 1980 Feb;92(2 Pt 1):149-55. doi: 10.7326/0003-4819-92-2-149.
5
Thrombotic thrombocytopenic purpura--coagulation parameters in twelve patients.血栓性血小板减少性紫癜——12例患者的凝血参数
Blood. 1973 Oct;42(4):499-507.
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Thrombotic thrombocytopenic purpura: analysis of 48 unselected cases.
Semin Thromb Hemost. 1980;6(4):341-9. doi: 10.1055/s-2007-1005107.
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Platelet-latelet-.血小板-血小板-
Arch Intern Med. 1977 Jun;137(6):735-7. doi: 10.1001/archinte.137.6.735.
8
[Thrombotic thrombocytopenic purpura. Spontaneous remission and remission concurrent with splenectomy and administration of ACTH, steroids and quinacrine].[血栓性血小板减少性紫癜。自发缓解以及与脾切除术、促肾上腺皮质激素、类固醇和奎纳克林给药同时出现的缓解]
Bol Med Hosp Infant Mex. 1960 Mar-Apr;17:199-213.
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Thrombotic thrombocytopenic purpura. Survival following treatment with aspirin, dipyridamole, and prednisone.血栓性血小板减少性紫癜。阿司匹林、双嘧达莫和泼尼松治疗后的生存情况。
JAMA. 1974 May 27;228(9):1141-3. doi: 10.1001/jama.228.9.1141.
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Role of splenectomy as a salvage procedure in thrombotic thrombocytopenic purpura.脾切除术作为血栓性血小板减少性紫癜挽救性治疗手段的作用。
Br J Surg. 1991 Nov;78(11):1389-90. doi: 10.1002/bjs.1800781139.

引用本文的文献

1
Thrombotic microangiopathy associated with infection.与感染相关的血栓性微血管病
BMJ Case Rep. 2018 Mar 17;2018:bcr-2017-222582. doi: 10.1136/bcr-2017-222582.
2
The role of splenectomy in the treatment of relapsing thrombotic thrombocytopenic purpura.
Ann Hematol. 1995 May;70(5):231-6.
3
Inhibition of platelet-aggregating activity in thrombotic thrombocytopenic purpura plasma by normal adult immunoglobulin G.正常成人免疫球蛋白G对血栓性血小板减少性紫癜血浆中血小板聚集活性的抑制作用。
J Clin Invest. 1984 Feb;73(2):548-55. doi: 10.1172/JCI111242.
4
Thrombotic thrombocytopenic purpura due to Mycoplasma pneumoniae.肺炎支原体所致血栓性血小板减少性紫癜
Postgrad Med J. 1992 May;68(799):393-4. doi: 10.1136/pgmj.68.799.393.
5
Thrombotic thrombocytopenic purpura (TTP) and splenectomy: a current appraisal.血栓性血小板减少性紫癜(TTP)与脾切除术:当前评估
Ann Surg. 1978 Nov;188(5):701-5. doi: 10.1097/00000658-197811000-00021.