Moncada G, Kobayashi Y, Maruyama Y, Kato T, Noda M, Kakuta T, Kishi Y, Numano F
Third Department of Internal Medicine, Tokyo Medical and Dental University.
Intern Med. 1998 Nov;37(11):934-9. doi: 10.2169/internalmedicine.37.934.
A 39-year-old woman was diagnosed by means of angiography as Takayasu arteritis complicated with severe systemic hypertension due to atypical coarctation of the aorta. Aorta-aortic bypass graft surgery was carried out successfully and hypertension remarkably improved. An evaluation of the graft 23 years later confirmed an almost perfect condition with a very satisfactory clinical status. Extensive long-term follow-up studies have been conducted among young people after surgical repair of aortic coarctation showing encouraging results, however the situation seems to be different for the atypical coarctation in Takayasu patients, since not only the age at the time of intervention affects the outcome, but the different circumstances mainly related to the natural history of the disease. We evaluated the long-term outcome based on similar cases with particular consideration to the extremely rare coexistence of familiar hypercholesterolemia.
一名39岁女性经血管造影诊断为大动脉炎合并主动脉非典型缩窄导致的严重全身性高血压。成功实施了主动脉-主动脉旁路移植手术，高血压明显改善。23年后对移植物的评估证实其状况几乎完美，临床状态非常令人满意。对主动脉缩窄手术修复后的年轻人进行了广泛的长期随访研究，结果令人鼓舞，然而，大动脉炎患者的非典型缩窄情况似乎有所不同，因为不仅干预时的年龄会影响结果，而且不同情况主要与疾病的自然史有关。我们基于类似病例评估了长期结果，并特别考虑了极其罕见的家族性高胆固醇血症共存情况。
