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良性对称性脂肪瘤病(马德隆病)。

Benign symmetric lipomatosis (Madelung's disease).

作者信息

Smith P D, Stadelmann W K, Wassermann R J, Kearney R E

机构信息

Division of General Surgery, University of South Florida, Tampa, USA.

出版信息

Ann Plast Surg. 1998 Dec;41(6):671-3. doi: 10.1097/00000637-199812000-00016.

DOI:10.1097/00000637-199812000-00016
PMID:9869144
Abstract

Benign symmetric lipomatosis, also known as Madelung's disease, is a rare condition characterized by massive fatty deposits arranged symmetrically around the neck, shoulders, and arms. These patients might present for liposuction and body contouring. Although infrequently encountered in the average plastic surgeon's practice, this condition should be considered when evaluating candidates for these procedures. The deformity is associated with chronic alcohol use and also with malignant tumors of the upper airways. The deformity is prone to recurrence and its surgical treatment often results in less than optimal aesthetic outcomes. Despite this fact, surgical removal via either direct excision or suction-assisted lipectomy provides the only real hope of palliation. This report describes a patient with this deformity and a review of the literature.

摘要

良性对称性脂肪瘤病,又称马德隆氏病,是一种罕见病症,其特征为在颈部、肩部和手臂周围对称分布的大量脂肪沉积。这些患者可能会因抽脂和身体塑形前来就诊。虽然普通整形外科医生在临床实践中很少遇到这种情况,但在评估这些手术的候选人时应考虑到这种病症。这种畸形与长期饮酒有关,也与上呼吸道恶性肿瘤有关。这种畸形容易复发,其手术治疗往往导致美学效果不尽人意。尽管如此,通过直接切除或吸脂辅助脂肪切除术进行手术切除仍是缓解病情的唯一真正希望。本报告描述了一名患有这种畸形的患者并对相关文献进行了综述。

相似文献

1
Benign symmetric lipomatosis (Madelung's disease).良性对称性脂肪瘤病(马德隆病)。
Ann Plast Surg. 1998 Dec;41(6):671-3. doi: 10.1097/00000637-199812000-00016.
2
Ultrasound assisted liposuction for the palliative treatment of Madelung's disease: a case report.超声辅助吸脂术用于马德隆氏病的姑息治疗:一例报告
Aesthetic Plast Surg. 2001 May-Jun;25(3):181-3. doi: 10.1007/s002660010118.
3
An aesthetic deformity: Madelung's disease.一种美学畸形:马德隆病。
Acta Otolaryngol. 2005 Mar;125(3):328-30. doi: 10.1080/00016480410022903.
4
[Rare case of Madelung disease].[马德隆病罕见病例]
Otolaryngol Pol. 2002;56(2):245-7.
5
Benign symmetric lipomatosis of the neck treated by liposuction. Case report.吸脂术治疗颈部良性对称性脂肪瘤。病例报告。
Scand J Plast Reconstr Surg Hand Surg. 1991;25(3):281-4. doi: 10.3109/02844319109020633.
6
[Madelung's disease. Clinical case and review of the literature].[马德隆氏病。临床病例及文献综述]
Minerva Chir. 1998 Jul-Aug;53(7-8):655-7.
7
[Benign symmetric lipomatosis (Madelung's disease): four cases report].[良性对称性脂肪瘤病(马德隆病):4例报告]
Lin Chuang Er Bi Yan Hou Tou Jing Wai Ke Za Zhi. 2015 Nov;29(21):1919-21.
8
Multiple symmetrical lipomatosis: A literature review and case report of a patient with Madelung's disease.多发性对称性脂肪瘤病:文献复习及一例马德隆病患者报告。
Pol Przegl Chir. 2023 Oct 13;96(0):130-134. doi: 10.5604/01.3001.0053.5997.
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[Madelung's disease (benign symmetric lipomatosis): still a mystery?].[马德隆病(良性对称性脂肪瘤病):仍是一个谜团?]
Praxis (Bern 1994). 2002 Jan 23;91(4):133-9. doi: 10.1024/0369-8394.91.4.133.
10
[Benign symmetrical lipomatosis. Lipectomy and liposuction in the treatment of Madelung disease].[良性对称性脂肪瘤病。脂肪切除术和抽脂术治疗马德隆病]
Handchir Mikrochir Plast Chir. 1992 Mar;24(2):93-6.

引用本文的文献

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A non-alcohol-related case of Madelung's disease: Challenging patient with progressive jugular vein distension.马德隆病的一例非酒精相关病例:伴有进行性颈静脉扩张的具有挑战性的患者。
Radiol Case Rep. 2021 Mar 19;16(5):1183-1187. doi: 10.1016/j.radcr.2021.02.050. eCollection 2021 May.
2
Imaging spectrum of abnormal subcutaneous and visceral fat distribution.皮下和内脏脂肪分布异常的影像学表现谱
Insights Imaging. 2020 Feb 13;11(1):24. doi: 10.1186/s13244-019-0833-4.
3
Case report of comorbid alcohol-induced psychotic disorder and Madelung's disease.
酒精所致精神障碍与马德隆病共病的病例报告
Shanghai Arch Psychiatry. 2014 Jun;26(3):160-4. doi: 10.3969/j.issn.1002-0829.2014.03.008.
4
Bilateral large palpable cervical masses: not always a malignant or infectious process.双侧可触及的颈部大肿块:并非总是恶性或感染性病变。
Bol Asoc Med P R. 2014;106(2):42-5.
5
Rare adipose disorders (RADs) masquerading as obesity.罕见脂肪组织疾病伪装成肥胖。
Acta Pharmacol Sin. 2012 Feb;33(2):155-72. doi: 10.1038/aps.2011.153.