Mevorah B, Orion E, de Viragh P, Bergman R, Gat A, Legume C, Van Neste D J, Brenner S
Department of Dermatology, Tel Aviv Sourasky Medical Center, Sackler Faculty of Medicine, Tel Aviv University, Tel Aviv, Israel.
Dermatology. 1998;197(4):373-6. doi: 10.1159/000018034.
A 13-year-old boy with typical peeling skin syndrome (PSS) is described. The clinical picture corresponded to the inflammatory variant of PSS (type B). In addition, the patient had gross and microscopic hair anomalies such as trichorrhexis invaginata-like changes, irregular hair shaft torsions and moniliform hair shaft diameter reductions. The observed dysmorphic hair changes are discussed and interpreted as being an integral component of the dermatosis in this case. To the best of our knowledge, such hair anomalies have not yet been described in PSS.
本文描述了一名患有典型剥脱性皮肤综合征（PSS）的13岁男孩。临床表现符合PSS的炎症变体（B型）。此外，该患者存在明显的和显微镜下可见的毛发异常，如套叠性脆发样改变、毛发干不规则扭转和念珠状毛发干直径变细。对观察到的毛发畸形变化进行了讨论，并解释为该病例中皮肤病的一个组成部分。据我们所知，PSS中尚未描述过此类毛发异常。
