Bernardis V, Sorrentino D, Snidero D, Avellini C, Paduano R, Beltrami C A, Digito F, Bartoli E
Gastrointestinal Unit, Department of Clinical and Experimental Pathology, University of Udine Medical School, Udine, Italy.
Digestion. 1999 Jan-Feb;60(1):82-5. doi: 10.1159/000007594.
The rare association between intestinal leiomyosarcoma, von Recklinghausen's disease (type-1 neurofibromatosis) and gastroparesis is described. A 20-year-old male, diagnosed 12 years earlier as having pelvic von Recklinghausen's disease, presented with nausea and vomiting. A gastric scintigraphy demonstrated an extremely slow gastric emptying time in the absence of obvious causes for gastroparesis. A small ileal leiomyosarcoma was later found and removed by surgery. The latter was followed by a marked improvement in the clinical condition of the patient.
本文描述了肠道平滑肌肉瘤、冯雷克林霍增氏病（1型神经纤维瘤病）和胃轻瘫之间的罕见关联。一名20岁男性，12年前被诊断患有盆腔冯雷克林霍增氏病，出现恶心和呕吐症状。胃闪烁扫描显示胃排空时间极慢，且无明显的胃轻瘫病因。后来发现一个小肠平滑肌肉瘤并通过手术切除。患者的临床状况随后有显著改善。
