Feig P U, Soter N A, Yager H M, Caplan L, Rosen S
JAMA. 1976 Nov 1;236(18):2065-8.
A patient with cutaneous necrotizing vasculitis had chronic urticaria associated with multiple system involvement including arthralgias, glomerulonephritis, myositis, pseudotumor cerebri, and adenopathy. Persistent hypocomplementemia is noted with classic pathway activation. The syndrome recognized in this patient and those few individuals reported previously seems to constitute a distinct category of collagen-vascular disease.
一名患有皮肤坏死性血管炎的患者伴有慢性荨麻疹，并累及多个系统，包括关节痛、肾小球肾炎、肌炎、假性脑瘤和淋巴结病。发现存在经典途径激活导致的持续性补体低下。该患者以及之前报道的少数个体所呈现的综合征似乎构成了一种独特的胶原血管病类型。
