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The genesis of cystic fibrosis lung disease.

作者信息

Wine J J

机构信息

Cystic Fibrosis Research Laboratory, Stanford University, Room 450, Bldg. 420, Main Quad, Stanford, California 94305-2130, USA.

出版信息

J Clin Invest. 1999 Feb;103(3):309-12. doi: 10.1172/JCI6222.

DOI:10.1172/JCI6222
PMID:9927490
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC407906/
Abstract
摘要

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本文引用的文献

1
The innate immune system in cystic fibrosis lung disease.囊性纤维化肺病中的先天性免疫系统。
J Clin Invest. 1999 Feb;103(3):303-7. doi: 10.1172/JCI6277.
2
Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease.囊性纤维化气道疾病发病机制中纤毛周围液体层耗竭而非离子组成异常的证据。
Cell. 1998 Dec 23;95(7):1005-15. doi: 10.1016/s0092-8674(00)81724-9.
3
cAMP-dependent absorption of chloride across airway epithelium.氯离子通过气道上皮细胞的环磷酸腺苷（cAMP）依赖性吸收。
Am J Physiol. 1998 Dec;275(6):L1219-27. doi: 10.1152/ajplung.1998.275.6.L1219.
4
Role of aquaporin water channels in kidney and lung.水通道蛋白水通道在肾脏和肺中的作用。
Am J Med Sci. 1998 Nov;316(5):310-20. doi: 10.1097/00000441-199811000-00004.
5
Loss of CFTR chloride channels alters salt absorption by cystic fibrosis airway epithelia in vitro.囊性纤维化跨膜传导调节因子（CFTR）氯离子通道的缺失会改变体外培养的囊性纤维化气道上皮细胞的盐分吸收。
Mol Cell. 1998 Sep;2(3):397-403. doi: 10.1016/s1097-2765(00)80284-1.
6
Evidence that Calu-3 human airway cells secrete bicarbonate.有证据表明Calu-3人呼吸道细胞分泌碳酸氢盐。
Am J Physiol. 1998 Mar;274(3):L450-3. doi: 10.1152/ajplung.1998.274.3.L450.
7
Inhibition of airway liquid secretion and its effect on the physical properties of airway mucus.气道液体分泌的抑制及其对气道黏液物理特性的影响。
Am J Physiol. 1998 Feb;274(2):L258-63. doi: 10.1152/ajplung.1998.274.2.L258.
8
Calcium-stimulated Cl- secretion in Calu-3 human airway cells requires CFTR.在Calu-3人呼吸道细胞中，钙刺激的氯离子分泌需要囊性纤维化跨膜传导调节因子（CFTR）。
Am J Physiol. 1997 Dec;273(6):L1208-19. doi: 10.1152/ajplung.1997.273.6.L1208.
9
Plasma membrane water permeability of cultured cells and epithelia measured by light microscopy with spatial filtering.通过空间滤波光学显微镜测量培养细胞和上皮细胞的质膜水渗透性。
J Gen Physiol. 1997 Sep;110(3):283-96. doi: 10.1085/jgp.110.3.283.
10
Cystic fibrosis transmembrane conductance regulator inverts protein kinase A-mediated regulation of epithelial sodium channel single channel kinetics.囊性纤维化跨膜传导调节因子反转蛋白激酶A介导的上皮钠通道单通道动力学调节。
J Biol Chem. 1997 May 30;272(22):14037-40. doi: 10.1074/jbc.272.22.14037.