Schlieter F, Szepan B, Polenz B
Klin Monbl Augenheilkd. 1976 Jun;168(6):788-93.
A patient aged 39 years with Wyburn-Mason syndrome is presented. He had an apple-sized intracranial arteriovenous angioma racemosum of the left temporo-medical region, which was inoperable, as it extended to the basal ganglia. It was diagnosed by carotid angiography and by sequential brain szintigraphy. More than 50 retinal arteriovenous anastomoses were observed in the left eye, involving all quadrants and the macular region. Some of these anastomoses were only found by fluorescence angiography. Clinical signs were hemiparesis and decreased sensibility of the right side, headaches, speech disorders and right homonymous hemianopia. Vision was decreased to 0.4. By partial embolisation via the right common carotid, it was possible to reduce the size of the intracranial hemangioma.
本文报告了一名39岁的Wyburn-Mason综合征患者。他左颞叶内侧区域有一个苹果大小的颅内葡萄状动静脉血管瘤，由于其延伸至基底神经节，无法进行手术。通过颈动脉血管造影和连续脑闪烁扫描得以确诊。左眼观察到50多处视网膜动静脉吻合，累及所有象限和黄斑区。其中一些吻合仅通过荧光血管造影发现。临床症状为偏瘫、右侧感觉减退、头痛、言语障碍和右侧同向性偏盲。视力降至0.4。通过右侧颈总动脉进行部分栓塞，有可能缩小颅内血管瘤的大小。
