Stepani P, Courouble Y, Postel P, Mezieres P, Tossou H, Couvelard A, Trophilme D, Barbare J C, Bories C
Service d'Hépato-Gastroentérologie, Centre Hospitalier, Beauvais.
Gastroenterol Clin Biol. 1998 Dec;22(12):1095-7.
We report a case of portal hypertension and neutrocytic ascites in a 52 year old man with POEMS syndrome. POEMS syndrome is an association of polyneuropathy, organomegaly, endocrinopathy, monoclonal gammapathy and skin changes. Portal hypertension is rare in POEMS syndrome and this is the first time that culture negative neutrocytic ascites has been described with this syndrome.
我们报告一例患有POEMS综合征的52岁男性患者出现门静脉高压和中性粒细胞性腹水。POEMS综合征是一种伴有多发性神经病、器官肿大、内分泌病、单克隆丙种球蛋白病和皮肤改变的综合征。门静脉高压在POEMS综合征中较为罕见,而这是首次报道该综合征伴有培养阴性的中性粒细胞性腹水。