Rubio Alcaide A, Herrero Platero C, Sánchez Calle J M, de Mora Martín M, Barakat S, Pinedo Rodríguez J, Conejo Muñoz L, Malpartida de Torres F
Servicio de Cardiología, Complejo Hospitalario Carlos Haya, Málaga.
Rev Esp Cardiol. 1999 Mar;52(3):211-4. doi: 10.1016/s0300-8932(99)74899-2.
Pericardial agenesis is a rare anomaly, difficult to diagnose. Its evolution is usually benign. However, on rare occasions, partial defects have been the cause of sudden death. Therefore, surgical treatment has sometimes been indicated, even though in the cases were asymptomatic. We report the case of a 50 year-old woman with partial pericardial agenesis and herniation of left atrial appendage trough. The defect was discovered by a routine chest x-ray and treated in a conservative way. Current diagnostic and therapeutic techniques are reviewed.
心包缺如是一种罕见的异常情况，诊断困难。其病情发展通常为良性。然而，在极少数情况下，部分缺损曾是猝死的原因。因此，有时即便患者无症状，也会考虑进行手术治疗。我们报告一例50岁女性患有部分心包缺如及左心耳经缺损处疝出的病例。该缺损通过常规胸部X线检查发现，并采取了保守治疗。本文对当前的诊断和治疗技术进行了综述。
