Croquet V, Aubé C, Pilette C, Fort J, Oberti F, Calès P, Ben Bouali A
Service d'Hépato-Gastroentérologie, CHU, Angers.
Gastroenterol Clin Biol. 1999 Feb;23(2):259-63.
We report a case of Budd-Chiari syndrome due to membranous obstruction of the inferior vena cava with a congenital malformation composed of a left inferior vena cava at the sub-renal level with an azygo-caval continuation without a retrohepatic segment of the inferior vena cava. To our knowledge, this is the first report of this association. The congenital venous malformation suggests a congenital etiology to the inferior vena cava membrane. The membranous obstruction was treated by percutaneous transluminal angioplasty. During the 10-year follow-up, there was no recurrence of the membranous obstruction as seen with Doppler ultrasound and magnetic resonance imaging.
我们报告一例因下腔静脉膜性梗阻导致的布加综合征,其合并一种先天性畸形,即肾下水平的左位下腔静脉,奇静脉-腔静脉延续,无肝后段下腔静脉。据我们所知,这是这种关联的首次报告。先天性静脉畸形提示下腔静脉膜存在先天性病因。膜性梗阻通过经皮腔内血管成形术治疗。在10年的随访中,经多普勒超声和磁共振成像检查,膜性梗阻未复发。