Tronnier V, Hartmann M, Hamer J, Kremer P, Sommer C, Jansen O, Kunze S
Department of Neurosurgery, University Hospital, Heidelberg College of Medicine.
Zentralbl Neurochir. 1999;60(2):86-92.
Two cases of predominantly extraspinally extra- and intradural spinal cord hemangioblastomas in two patients each with and without von Hippel-Lindau-disease are reported. Preoperative MRI and angiographic findings are presented and the differential diagnosis is discussed. The surgical procedure is described and the literature of hemangioblastomas in this rare localization is reviewed. Improvements in both radiologic diagnosis and microsurgical techniques, and consequent screening programs will enhance life expectancy in patients afflicted with von Hippel-Lindau disease.
报告了两例主要位于脊髓外硬膜外和硬膜内的血管母细胞瘤病例，两名患者分别患有和未患有冯·希佩尔-林道病。介绍了术前MRI和血管造影结果，并讨论了鉴别诊断。描述了手术过程，并回顾了这种罕见部位血管母细胞瘤的文献。放射学诊断和显微外科技术的改进以及随之而来的筛查计划将提高冯·希佩尔-林道病患者的预期寿命。
