Riantawan P, Yodtasurodom C, Chotivatanapong T, Subhannachart P
Division of Medicine, Central Chest Hospital, Nonthaburi, Thailand.
J Med Assoc Thai. 1999 Mar;82(3):312-6.
A young man presented with prolonged pyrexia, recurrent optic neuritis, thrombophlebitis and bilateral pulmonary artery aneurysms with thrombus formation. The life-threatening hemoptysis necessitated mechanical ventilatory support and emergency left lower lobectomy. Systemic corticosteroids conferred clinical improvement and reduction of the remaining right pulmonary artery aneurysm. The patient eventually succumbed to sudden massive hemoptysis. This report underscores the unpredictable nature of this syndrome and emphasises the need for aggressive surgical intervention of pulmonary artery aneurysms in Hughes-Stovin syndrome.
一名年轻男性出现长期发热、复发性视神经炎、血栓性静脉炎以及伴有血栓形成的双侧肺动脉瘤。危及生命的咯血需要机械通气支持和急诊左下叶切除术。全身使用皮质类固醇使临床症状改善，剩余的右肺动脉瘤缩小。患者最终死于突然大量咯血。本报告强调了该综合征的不可预测性，并强调了对Hughes-Stovin综合征中肺动脉瘤进行积极手术干预的必要性。
