Nishi K, Myou S, Ooka T, Taitou H, Fujimura M, Matsuda T
Division of Pulmonary Medicine, Ishikawa Prefectural Central Hospital, Kanazawa, Japan.
Nihon Kyobu Shikkan Gakkai Zasshi. 1993 Mar;31(3):379-84.
A 27-year-old man suffering from incomplete type of Behçet's disease presented with swelling of the left thigh. Venography showed obstruction of the left femoral vein by thrombus, and he was diagnosed as having deep vein thrombosis of the left femoral vein. The next year, he developed recurrent hemoptysis. Pulmonary angiography showed aneurysm and mural thrombosis of the left pulmonary artery. Fiberoptic bronchoscopy showed a reddish eminence of the left Behçet bronchus, suggestive of broncho-pulmonary artery fistula. After treatment with colchicine, the hemoptysis decreased. We report a very rare case of Behçet's disease presenting with Hughes-Stovin syndrome.
一名患有不完全型白塞病的27岁男性出现左大腿肿胀。静脉造影显示左股静脉被血栓阻塞,他被诊断为左股静脉深静脉血栓形成。次年,他出现反复咯血。肺血管造影显示左肺动脉有动脉瘤和壁内血栓形成。纤维支气管镜检查显示左白塞支气管有红色隆起,提示支气管-肺动脉瘘。经秋水仙碱治疗后,咯血减少。我们报告了一例非常罕见的以休斯-斯托文综合征为表现的白塞病病例。