Herb S, Hetzel M, Hetzel J, Friedrich J, Weber J
Dept of Internal Medicine II, University of Ulm, Germany.
Eur Respir J. 1998 May;11(5):1191-3. doi: 10.1183/09031936.98.11051191.
In 1959 HUGHES and STOVIN described a syndrome consisting of multiple pulmonary aneurysms and peripheral venous thrombosis. Since that time several cases of the Hughes-Stovin syndrome have been published. We present the case of a 25 yr old man who, in addition to the classical symptoms, had multiple aneurysms of the bronchial arteries, which were the cause of severe haemoptysis. An aneurysm of the left hepatic artery was also detected. To our knowledge this is the first description of aneurysms of the bronchial arteries in Hughes-Stovin syndrome. Bleeding was successfully treated by double embolization of bronchial arteries via transfemoral catheter.
1959年,休斯和斯托文描述了一种由多发性肺动脉瘤和外周静脉血栓形成组成的综合征。自那时以来,已发表了几例休斯 - 斯托文综合征病例。我们报告一例25岁男性病例,该患者除了具有典型症状外,还存在多条支气管动脉的动脉瘤,这是严重咯血的原因。还检测到左肝动脉有一个动脉瘤。据我们所知,这是休斯 - 斯托文综合征中支气管动脉动脉瘤的首次描述。通过经股动脉导管对支气管动脉进行双重栓塞成功治疗了出血。