Cherradi N, Jelthi A, Alhamany Z, Miri A, Forest M
Service d'Anatomie Pathologique, Hôpital d'Enfants de Rabat, CHU, Rabat-Salé, Maroc, Paris.
Clin Exp Pathol. 1999;47(5):249-55.
Fibrocartilaginous mesenchymoma of bone is a tumoral entity which is somewhat controversial. It has been delineated in 1984 by Dahlin and al. Fifteen cases have been reported in the literature. We report a new case which involves proximal humerus. X-ray data, microscopic findings and local recurrence indicate a low grade malignancy. Metastasis have never been reported. The main differential diagnosis are desmoplastic fibroma, fibrous dysplasia and fibrosarcoma with low grade malignancy. Treatment is surgical.
骨纤维软骨间叶瘤是一种存在一定争议的肿瘤实体。它于1984年由达林等人首次描述。文献中已报道了15例病例。我们报告1例累及肱骨近端的新病例。X线检查结果、显微镜下表现及局部复发提示为低级别恶性肿瘤。尚未有转移的报道。主要鉴别诊断包括促结缔组织增生性纤维瘤、骨纤维异常增殖症和低级别恶性纤维肉瘤。治疗方式为手术治疗。