Gedikoglu G, Aksoy M C, Ruacan S
Department of Pathology, Hacettepe University Medical Faculty, 06530 Beysukent, Ankara, Turkey.
Pathol Int. 2001 Aug;51(8):638-42. doi: 10.1046/j.1440-1827.2001.01247.x.
A case of a 9-year-old boy with fibrocartilaginous mesenchymoma located in the distal femur is presented. Fibrocartilaginous mesenchymoma is a rare tumor. There have been 17 cases reported since 1984. The presenting complaint was pain and local discomfort. Radiological examination showed lytic and sclerotic lesions located in the distal femur. Magnetic resonance imaging showed that there was no soft tissue expansion. Differential diagnosis included fibrocartilaginous dysplasia, dedifferentiated chondrosarcoma, desmoplastic fibroma, fibrosarcoma and low-grade osteosarcoma. The diagnosis of the tumor in a state hospital would not have been possible. Wide resection of the tumor and resection arthrodesis with an intramedullary nail has yielded good results. The patient has been disease free for 4 years. Pathological diagnosis of this very rare tumor may be challenging; the treatment should be wide resection of the tumor.
本文报告了一例9岁男孩，其纤维软骨间叶瘤位于股骨远端。纤维软骨间叶瘤是一种罕见肿瘤。自1984年以来，已有17例相关病例报道。主要症状为疼痛和局部不适。放射学检查显示股骨远端有溶骨性和硬化性病变。磁共振成像显示无软组织扩张。鉴别诊断包括纤维软骨发育异常、去分化软骨肉瘤、促结缔组织增生性纤维瘤、纤维肉瘤和低级别骨肉瘤。在一家公立医院不可能对该肿瘤进行诊断。肿瘤广泛切除并使用髓内钉进行切除关节固定术取得了良好效果。该患者已无病生存4年。对这种极为罕见的肿瘤进行病理诊断可能具有挑战性；治疗应采取肿瘤广泛切除。
