Masquijo Julio Javier, Sartori Federico, Innocenti Sergio
Departamento de Ortopedia y Traumatología Infantil, Sanatorio Allende, Córdoba, Argentina.
Hospital Juan P. Garrahan, Buenos Aires, Argentina.
Arch Argent Pediatr. 2014 Oct;112(5):e222-6. doi: 10.5546/aap.2014.e222.
Fibrocartilaginous mesenchymoma (FCM) is a rare tumor that primarily affects the long bones. Few cases have been reported since its description. A case of a 4-year-old boy with FCM located in the humerus is presented. Radiological examination showed an expansive lytic lesion located in the metaphyseal proximal humerus. Magnetic resonance imaging showed soft tissue expansion. Histopathological diagnosis was confirmatory of FCM. Curettage, adjuvant phenolization, and bone grafting with bone substitute, and autologous bone marrow was performed. During a follow-up period of 2 years, there was no evidence of disease progression. FCM should be considered in the differential diagnosis of lytic bone lesions in children and adolescents.
纤维软骨性间叶瘤(FCM)是一种罕见的肿瘤,主要累及长骨。自其被描述以来,报道的病例很少。本文介绍了一例4岁男孩患肱骨FCM的病例。放射学检查显示肱骨近端干骺端有一个膨胀性溶骨性病变。磁共振成像显示软组织扩张。组织病理学诊断确诊为FCM。进行了刮除、辅助酚化、骨替代物植骨和自体骨髓移植。在2年的随访期内,没有疾病进展的证据。在儿童和青少年溶骨性骨病变的鉴别诊断中应考虑FCM。