Martínez-Lage Juan F, Alarcón Fernando, Hernández-Barceló José E, Almagro María-José, Alfaro Raúl, Galera-Miñarro Ana
Regional Service of Neurosurgery, Virgen de la Arrixaca University Hospital, 30120, El Palmar, Murcia, Spain.
Childs Nerv Syst. 2010 Mar;26(3):385-9. doi: 10.1007/s00381-009-1042-0.
Originally described by Dahlin et al. in 1984, fibrocartilaginous mesenchymoma (FCM) constitutes a rare bone tumor of children and adolescents that mainly affects the long bones. A spinal location of this tumor is exceptional. Only two previous instances of vertebral FCM have been reported in the current literature, and both occurred in young adults.
We report the case of a 9-year-old boy with backache caused by a neoplasm that involved the Th12 vertebra treated with tumor excision. Histopathological diagnosis was confirmatory of FCM. During a follow-up period of 2 years, there was no evidence of disease progression. Our patient, thus, represents the first case of FCM occurring in a child.
Given the rarity of spinal FCM, there are no guidelines about its management. However, treatment of this neoplasm seems to be mainly surgical aiming at total removal of the lesion, if feasible, as FCM may recur locally.
纤维软骨性间叶瘤（FCM）最初由达林等人于1984年描述，是一种罕见的儿童和青少年骨肿瘤，主要累及长骨。该肿瘤发生于脊柱的情况极为罕见。目前文献中仅报道过两例椎体FCM，且均发生于年轻成年人。
我们报告一例9岁男孩，因肿瘤累及胸12椎体导致背痛，接受了肿瘤切除术。组织病理学诊断确诊为FCM。在2年的随访期内，无疾病进展迹象。因此，我们的患者代表了首例发生于儿童的FCM病例。
鉴于脊柱FCM的罕见性，目前尚无关于其治疗的指南。然而，该肿瘤的治疗似乎主要是手术治疗，目标是在可行的情况下彻底切除病变，因为FCM可能会局部复发。
