Solitary fibrous tumor of the orbit: a poorly-recognized orbital lesion.

PURPOSE

The authors report three cases with solitary fibrous tumor (SFT) of the orbit with variable clinical presentation.

METHODS

The authors identified three patients with a diagnosis of SFT, and clinical histories, radiographs and pathologic specimens were reviewed.

RESULTS

Two SFTs are reported arising in the lacrimal gland fossa of a 24-year-old male and a 26-year-old female and a retrobulbar SFT is reported occurring in a 40-year-old female. While two patients had slow growth histories, one patient had a history of rapid progression. Immunohistochemically, the tumor cells were strongly positive for CD34 in all three cases.

CONCLUSION

The clinical presentation of the orbital SFT may be varied. Immunohistochemical analysis may help in the diagnosis of solitary fibrous tumor and the treatment is en bloc excision. A careful follow-up is necessary because it may recur years after excision of the primary tumor.