Brochériou I, Quillard A, Gatecel C, Wassef M
Service d'Anatomie et de Cytologie Pathologiques, Hôpital Pitié-Salpêtrière, 47-82, bd de l'Hôpital, 75013 Paris.
Ann Pathol. 2000 Jan;20(1):69-72.
Primary sarcomas of great vessels are rare and involve the aorta, pulmonary artery and inferior vena cava. The pathologic classification of these tumors can be made on the location of the sarcoma in relation to the vessel wall, luminal or mural. Luminal sarcomas are usually intimal sarcoma and mural sarcoma are most frequently leiomyosarcoma. The myofibroblastic or endothelial differentiation of these tumors is still debated. We report a case of intimal sarcoma of the pulmonary artery.
大血管原发性肉瘤较为罕见，累及主动脉、肺动脉和下腔静脉。这些肿瘤的病理分类可根据肉瘤相对于血管壁的位置进行，分为腔内型或壁内型。腔内肉瘤通常为内膜肉瘤，壁内肉瘤最常见的是平滑肌肉瘤。这些肿瘤的肌成纤维细胞或内皮分化仍存在争议。我们报告一例肺动脉内膜肉瘤病例。
