Walters H L, Mavroudis C, Tchervenkov C I, Jacobs J P, Lacour-Gayet F, Jacobs M L
Department of Surgery, Wayne State University School of Medicine, Children's Hospital of Michigan, Detroit 48201, USA.
Ann Thorac Surg. 2000 Apr;69(4 Suppl):S249-63. doi: 10.1016/s0003-4975(99)01247-3.
Double outlet right ventricle (DORV) is a type of ventriculoarterial connection in which both great vessels arise entirely or predominantly from the right ventricle. Although the presence of aortic-mitral discontinuity and bilateral coni are important descriptors, they should not serve as absolute prerequisites for the diagnosis of DORV. The morphology of DORV is encompassed by a careful description of the ventricular septal defect (VSD) with its relationship to the semilunar valves, the great artery relationships to each other, the coronary artery anatomy, the presence or absence of pulmonary outflow tract obstruction (POTO) and aortic outflow tract obstruction (AOTO), the tricuspid-pulmonary annular distance, and the presence or absence of associated cardiac lesions. The preferred surgical treatment involves the connection of the left ventricle to the systemic circulation by an intraventricular tunnel repair connecting the VSD to the systemic semilunar valve. This ideal surgical therapy is not always possible due to the presence of confounding anatomical barriers. A multitude of alternative surgical procedures has been devised to accommodate these more complex situations. A framework for the development of the DORV module for a pediatric cardiac surgical database is proposed.
右心室双出口（DORV）是一种心室动脉连接类型，其中两根大动脉全部或主要起源于右心室。尽管主动脉-二尖瓣不连续和双侧圆锥的存在是重要的描述特征，但它们不应作为诊断DORV的绝对先决条件。DORV的形态包括对室间隔缺损（VSD）及其与半月瓣的关系、大动脉相互之间的关系、冠状动脉解剖结构、有无肺动脉流出道梗阻（POTO）和主动脉流出道梗阻（AOTO）、三尖瓣-肺动脉环距离以及有无相关心脏病变的仔细描述。首选的手术治疗方法是通过将VSD与体循环半月瓣相连的室内隧道修复术，使左心室与体循环相连。由于存在复杂的解剖屏障，这种理想的手术治疗并非总是可行。人们已经设计了多种替代手术方法来适应这些更复杂的情况。本文提出了一个用于儿科心脏手术数据库的DORV模块开发框架。
