Häusler M, Meilicke R, Biesterfeld S, Kentrup H, Friedrichs F, Kusenbach G
Department of Pediatrics, University Hospital, RWTH Aachen, Germany.
Respiration. 2000;67(3):316-9. doi: 10.1159/000029517.
Organizing pneumonia in cystic fibrosis has hitherto been considered a nonspecific reparative process. We report on an adult patient with cystic fibrosis and histologically proven bronchiolitis obliterans organizing pneumonia, who experienced sustained clinical improvement under corticosteroid therapy. This case suggests that bronchiolitis obliterans organizing pneumonia may be a distinct pulmonary complication in cystic fibrosis and improve with specific therapy.
迄今为止，囊性纤维化中的机化性肺炎一直被认为是一种非特异性修复过程。我们报告了一例成年囊性纤维化患者，经组织学证实为闭塞性细支气管炎伴机化性肺炎，该患者在皮质类固醇治疗下临床持续改善。该病例提示，闭塞性细支气管炎伴机化性肺炎可能是囊性纤维化中一种独特的肺部并发症，且可通过特定治疗得到改善。
