Kianmanesh Rad A R, Vilotte J, Benhamou G
Service de Chirurgie Générale et Digestive, Hôpital Bichat-Claude-Bernard, Paris.
Ann Chir. 1997;51(9):995-1000.
Pneumatosis cystoides intestinalis (PCI) is a rare entity in which gas is found in cysts located in the intestinal wall. PCI is a sign, not a disease; therefore, its relevance should be interpreted within the whole clinical context. PCI has been found in several distinctive clinical settings, which the authors review in the light of their 3 new cases. Morphologic and endoscopic examinations showed "polypoid" intraluminal formations corresponding to pneumocysts which should not be misdiagnosed with a diffuse polyposis. The most important tasks of the physician include: 1) recognition of the entity of PCI so that patients are not misdiagnosed and mismanaged as having malignancy or polyposis; and 2) differentiation of the benign noncomplicated cases from life-threatening forms (bowel necrosis, perforation, and infections), in which immediate surgery is necessary, and which are associated with high mortality.
肠壁囊样积气症(PCI)是一种罕见病症,即在肠壁囊肿中发现气体。PCI是一种体征,而非疾病;因此,其相关性应在整个临床背景下解读。PCI已在多种独特的临床环境中被发现,作者根据其三例新病例对此进行了综述。形态学和内镜检查显示“息肉样”腔内结构对应于肺囊肿,不应误诊为弥漫性息肉病。医生的最重要任务包括:1)识别PCI实体,以免患者被误诊为恶性肿瘤或息肉病并得到不当治疗;2)区分良性非复杂病例与危及生命的类型(肠坏死、穿孔和感染),后者需要立即手术,且死亡率很高。