Dembinski J, Kaminski M, Schild R, Kuhl C, Hansmann M, Bartmann P
Department of Neonatology, University of Bonn, Germany.
Am J Perinatol. 1999;16(10):509-14. doi: 10.1055/s-1999-7286.
Approximately 50% of all congenital lung malformations are pulmonary and mediastinal bronchogenic cysts (BC). Therefore, their diagnosis and management is of clinical importance. Usually asymptomatic in the first months of life, bronchogenic cysts are frequently clinically inapparent even adulthood. Early diagnosis and elective surgery can prevent late complications such as pneumothorax, pulmonary hypertension, and recurrent infections; prognosis after surgery is excellent. If mediastinal shifting is present, fetal thoracocentesis is indicated to prevent cardiovascular insufficiency. We report a case of a prenatally diagnosed intrapulmonary BC of the right lung. Following in utero thoracocentesis of the cyst and transient spontaneous regression postnatal onset of severe clinical symptoms due to rapidly developing hyperinflation and mediastinal shifting within the first days of life required early surgical intervention.
所有先天性肺畸形中约50%是肺和纵隔支气管源性囊肿（BC）。因此，其诊断和处理具有临床重要性。支气管源性囊肿在生命的最初几个月通常无症状，甚至在成年期也常常无明显临床症状。早期诊断和择期手术可预防气胸、肺动脉高压和反复感染等晚期并发症；手术预后良好。如果出现纵隔移位，则需进行胎儿胸腔穿刺术以预防心血管功能不全。我们报告1例产前诊断为右肺肺内BC的病例。在对囊肿进行宫内胸腔穿刺术后，出生后由于出生后数天内迅速发展的肺过度充气和纵隔移位，出现严重临床症状并短暂自发消退，需要早期手术干预。
