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高嗜酸性粒细胞综合征:14例病例分析并文献复习

The hypereosinophilic syndrome: analysis of fourteen cases with review of the literature.

作者信息

Chusid M J, Dale D C, West B C, Wolff S M

出版信息

Medicine (Baltimore). 1975 Jan;54(1):1-27.

PMID:1090795
Abstract

Several closely related disease entities make up the idiopathic hypereosinophilic syndrome (HES). The syndrome is manifest by persistent and prolonged eosinophilia with organ damage. A group of 14 patients had hematologic, cardiac, and neurologic abnormalities attributable to this disease. Patient survival and response to chemotherapy was significantly better in this group than in previously reported patients. The etiology of HES remains unknown, as does the mechanism of tissue damage.

摘要

几种密切相关的疾病实体构成了特发性嗜酸性粒细胞增多综合征(HES)。该综合征表现为持续性和长期性嗜酸性粒细胞增多并伴有器官损害。一组14例患者出现了可归因于该疾病的血液学、心脏和神经学异常。该组患者的生存率和对化疗的反应明显优于先前报道的患者。HES的病因仍然不明,组织损伤机制也同样未知。

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