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患有迈耶-罗基坦斯基-库斯特-豪泽综合征患者的腹腔镜子宫肌瘤切除术

Laparoscopic myomectomy in a patient with Mayer-Rokitansky-Kuster-Hauser syndrome.

作者信息

Tsin D A, Waters T K, Granato R C

机构信息

Department of Obstetrics and Gynecology, Flushing Hospital Medical Center, Queens, NY, USA.

出版信息

J Am Assoc Gynecol Laparosc. 2000 Aug;7(3):411-3. doi: 10.1016/s1074-3804(05)60488-4.

Abstract

A 36-year-old woman had primary amenorrhea, pelvic pain, Mayer-Rokitansky-Kuster-Hauser syndrome, and an 8.5-cm, solid pelvic mass. The leiomyoma uteri was removed laparoscopically from the vestigial mullerian duct with secondary vaginopoiesis. The patient had a satisfactory clinical outcome. Finding of a leiomyoma in a patient with Rokitansky syndrome is rare. To our knowledge this is the first such case in which the myoma was removed by laparoscopy.

摘要

一名36岁女性患有原发性闭经、盆腔疼痛、迈耶-罗基坦斯基-库斯特-豪泽综合征,盆腔有一个8.5厘米的实性肿块。通过腹腔镜从残留的苗勒管切除平滑肌瘤并行二期阴道成形术。患者临床结局满意。在罗基坦斯基综合征患者中发现平滑肌瘤很罕见。据我们所知,这是首例通过腹腔镜切除肌瘤的此类病例。

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