Leiomyomas in both uterine remnants in a woman with the Mayer-Rokitansky-Küster-Hauser syndrome.

OBJECTIVE

To describe a case of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome associated with bilateral myomas in uterine remnants.

DESIGN

Case report.

SETTING

University hospital.

PATIENT(S): A 35-year-old woman with MRKH syndrome and pelvic pain, in whom leiomyomas were diagnosed by imaging techniques.

INTERVENTION(S): Diagnostic laparoscopy followed by excision of leiomyomas and uterine remnants by laparotomy.

MAIN OUTCOME MEASURE(S): Resolution of symptoms and histologic confirmation of the clinic diagnosis.

RESULT(S): After a 6-month follow-up period, the patient was asymptomatic. The histologic examination confirmed MRKH syndrome associated with multiple myomas in both rudimentary uteri.

CONCLUSION(S): This is an unusual case of MRKH syndrome associated with bilateral leiomyomas. The excision of the tumors with the adjacent uterine remnants is indicated when they are symptomatic.