Lanowska Malgorzata, Favero Giovanni, Schneider Achim, Köhler Christhardt
Department of Gynecology, Charite Universitätsmedizin, Berlin, Germany.
Fertil Steril. 2009 Mar;91(3):931.e17-8. doi: 10.1016/j.fertnstert.2008.09.057. Epub 2008 Nov 6.
To report a rare case of a myoma simulating a pelvic tumor in a patient with Mayer-Rokitanski-Küster-Hauser (MRKH) syndrome. The rudimentary uterus may develop fibroids, and this event can lead to problems in differential diagnosis, especially if no vaginal reconstruction has been carried out.
Case-report.
University hospital.
PATIENT(S): A 39-year-old patient with MRKH syndrome presented with a solid pelvic mass 9 cm in diameter on ultrasound and magnetic resonance imaging that could not be differentiated between fibroid and ovarian tumor.
INTERVENTION(S): The patient was laparoscopically operated, and a fibroid of the right uterine residual was detected and removed.
RESULT(S): Histology confirmed a benign leiomyoma.
CONCLUSION(S): In patients with MRKH syndrome, laparoscopy allows analysis of the origin of a solid pelvic tumor and its removal. Especially in patients without vaginal reconstruction, laparoscopy may be superior to imaging techniques.
报告1例患有迈耶-罗基坦斯基-库斯特-豪泽综合征(MRKH综合征)的患者,其肌瘤模拟盆腔肿瘤的罕见病例。残角子宫可能会发生子宫肌瘤,这一情况会导致鉴别诊断出现问题,尤其是在未进行阴道重建的情况下。
病例报告。
大学医院。
一名39岁的MRKH综合征患者,超声和磁共振成像显示盆腔有一个直径9厘米的实性肿块,无法区分是肌瘤还是卵巢肿瘤。
对患者进行腹腔镜手术,检测并切除了右侧子宫残端的一个肌瘤。
组织学证实为良性平滑肌瘤。
对于患有MRKH综合征的患者,腹腔镜检查可用于分析盆腔实性肿瘤的来源并将其切除。特别是对于未进行阴道重建的患者,腹腔镜检查可能优于成像技术。