Tazi K, Moudouni S, Koutani A, Ibn Attya A, Hachimi M, Lakrissa A
Service d'Urologie B, CHU Ibn Sina, Rabat, Maroc.
Prog Urol. 2000 Jun;10(3):469-72.
The authors report a case of paratesticular thabdomyosarcoma in a young adult. This tumour is more frequent in children than in adults. Rhabdomyosarcoma is the commonest variety of soft tissue sarcoma in children and young adults. It represents 6.5% of all malignant tumours in paediatrics with an annual incidence of 4 to 7 cases/million children. The primary paratesticular site is considered to have a good prognosis in comparison with other rhabdomyosarcomas, despite the frequency of retroperitoneal lymph node invasion. This superficial site allows rapid diagnosis and consequently often complete resection of the tumour. The multidisciplinary treatment of paratesticular rhabdomyosarcoma has improved control of the disease with a 2-year survival of 80%.
作者报告了一例发生在青年男性的睾丸旁横纹肌肉瘤病例。该肿瘤在儿童中比在成人中更常见。横纹肌肉瘤是儿童和青年中最常见的软组织肉瘤类型。它占儿科所有恶性肿瘤的6.5%，年发病率为每百万儿童4至7例。尽管腹膜后淋巴结转移常见，但与其他横纹肌肉瘤相比，睾丸旁原发部位被认为预后良好。这个浅表部位便于快速诊断，因此肿瘤常常能完整切除。睾丸旁横纹肌肉瘤的多学科治疗改善了疾病控制，2年生存率达80%。
